Creutzfeldt-Jakob disease

Among prion diseases, Creutzfeldt-Jakob disease is a neurodegenerative disorder primarily characterized by dementia and balance problems. The disease progresses rapidly and is invariably fatal.

Our Mission

  • Monitoring the epidemiological trends of Creutzfeldt-Jakob disease in collaboration with the National Creutzfeldt-Jakob Disease Surveillance Network (RSN-MCJ)

  • Informing the general public

  • Provide insights to health authorities

In brief

Videos, infographics, key statistics, expert interviews… Find the latest news and key information on Creutzfeldt-Jakob disease here

vMCJ

(a variant of Creutzfeldt-Jakob disease), a foodborne prion disease, emerged in Great Britain in 1996

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Cases of vCJD were diagnosed in France between 1992 and 2019. The last known French case of vCJD died in 2019.

The disease

Creutzfeldt-Jakob Disease in France

Creutzfeldt-Jakob disease (CJD) is a neurodegenerative disease caused by the accumulation of an abnormal prion protein in the brain. It occurs in three epidemiological forms:

  • The most common form is known as sporadic. It affects individuals of both sexes...

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What We Do

The primary objective of the epidemiological surveillance of CJD conducted by Santé publique France is to monitor trends in vCJD cases and the effectiveness of the measures implemented (ban on the use of meat-and-bone meal in cattle feed). In addition, the surveillance aims to detect the...

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Data

View data on the epidemiological situation of Creutzfeldt-Jakob disease in France on Santé publique France

The surveillance system for Creutzfeldt-Jakob disease, based on mandatory reporting and notifications to the RNS-CJD, makes it possible to track the progression of this disease

The emergence of the variant form of CJD and its link to bovine spongiform encephalopathy (BSE)

Following the...

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Publications

Here you will find the latest scientific publications related to the studies and research conducted by Santé publique France.

2 publications